J Clin Endocrin Metab. 2008 Jan 22; doi:10.1210/jc.2007-1701
"Activation of peroxisome proliferator activated receptor pathway stimulates the mitochondrial repiratory chain and can correct deficiencies in patients' cells lacking its components."

Plos Bio. 2007 Oct;5(10):e259.
"Relationship Between Mitochondrial Electron Transport Chain Dysfunction, Development, and Life Extension in Caenorhabditis elegans ."

PloS One 2007 Oct;2(10):e1066.
"Hsp90 Inhibition Decreases Mitochondrial Protein Turnover."

EMBO Journal 2007 Sept;26:4335-46.
"Coa1 links the Mss51 post-translational function to Cox1 cofactor insertion in cytochrome c oxidase assembly."

J. Bio. Chem. 2007 Aug;282(32):23613-21.
"Compartment-specific Phosphorylation of Phosducin in Rods Underlies Adaptation to Various Levels of Illumination."

Genome Res. 2007 Aug;17:1319-1326.
"Direct linkage of mitochondrial genome variation to risk factors for type 2 diabetes in conplastic strains."

J Biol Chem. 2007 Aug;doi:10.1074/jbc.M703528200
"Early developmental pathology due to cytochrome c oxidase deficiency is revealed by a new zebrafish model."

J Bio. Chem. 2007 June;282(24):17557-62.
"An Assembled Complex IV Maintains the Stability and Activity of Complex I in Mammalian Mitochondria."

Biochimica et Biophysica Acta 2007 May;1772:533-42.
"Yeast NDI1 improves oxidative phosphorylation capacity and increases protection against oxidative stress and cell death in cells carrying a Leber's hereditary optic neuropathy mutation ."

Neurosci. Letters 2007 Apr;416:160-4.
"Ethanol withdrawal posttranslationally decreases the activity of cytochrome c oxidase in an estrogen reversible manner."

Nature Gen. 2007 Mar;39:534-9.
"Mitochondrial aspartyl-tRNA synthetase deficiency causes leukoencephalopathy with brain stem and spinal cord involvement and lactate elevation."

Hum Molec Genetics. 2007 Jan 8;16(4):431-44.
"Increased longevity and refractoriness to Ca2+ -dependent neurodegeneration in Surf1 knockout mice."

Invest. Ophthal. and Visual Sci. 2007;48:5091-100..
"Crucial Role of Apoptosis in the Resolution of Experimental Autoimmune Anterior Uveitis."

J Bioenerg Biomembr. 2006 Dec;38(5-6):283-91
"Cytochrome c oxidase subunit IV is essential for assembly and respiratory function of the enzyme complex."

Mol Biol Cell. 2006 Aug
"ATP-binding cassette transporters are required for efficient RNA interference in Caenorhabditis elegans."

J Biol Chem. 2006 Jul 6
"Human mitochondrial DNA nucleoids are linked to protein folding machinery and metabolic enzymes at the mitochondrial inner membrane."

Biochim Biophys Acta. 2006 Feb;1757(2):115-22
"Riboflavin enhances the assembly of mitochondrial cytochrome c oxidase in C. elegans NADH-ubiquinone oxidoreductase mutants."

J Clin Invest. 2005 Oct;115(10):2784-92.
"A molecular chaperone for mitochondrial complex I assembly is mutated in a progressive encephalopathy."

Nucleic Acids Res. 2006 Aug;34(13):e95
"Production of transmitochondrial cybrids containing naturally occurring pathogenic mtDNA variants."

Image of the CcoI antibody (green) used to stain MELAS (myoclonus, epilepsy, lactic acidosis and stroke like episodes) where a mutation in a mitochondrially-encoded tRNA gene alters the biogenesis of Cco. A noted difference in staining can be seen between cells which have the CcoI subunit and those which either have little to none of the subunit present. The antibody was used at 7.5 ug/mL of anti-Cco subunit 1 mAb (MS404) in 10% goat serum, overnight at 4°C, when testing fibroblasts or other adherent cells.