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Carbamoyl-phosphate synthase I (CPS1)

UniProt Number: P31327
Alternate Names: carbamoyl-phosphate synthetase I, CPSase I
Structure and Function: Involved in the urea cycle where the enzyme plays an important role in removing excess ammonia from the cell.
Disease Associations: Defects in CPS1 are the cause of carbamoyl phosphate synthetase 1 deficiency (CPS1D) [MIM:237300]. Defects in CPS1 are are also associated with susceptibility to familial persistent pulmonary hypertension of the newborn [MIM:265380]; also called congenital alveolar capillary dysplasia or CACD.

Monoclonal Antibodies
Cat. No. Name Reactivity Apps. Amount
MS738 CPS1 antibody human ICC, IP, FLOW 100 µg

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